Tetralogy of Fallot (pronounced te-tral-uh-jee of Fal-oh) is a birth defect that affects normal blood flow through the heart. It happens when a babys heart does not form correctly as the baby grows and develops in the mothers womb during pregnancy.
How do you explain tetralogy of Fallot to parents?
Tetralogy of Fallot (fah-LO) is a congenital (present at birth) heart defect. In tetralogy of Fallot (TOF), four related heart defects change the way blood flows to the lungs and through the heart. TOF is repaired through open-heart surgery soon after birth or later in infancy.
What are the 4 abnormalities in tetralogy of Fallot?
Tetralogy of Fallot is a combination of four congenital heart defects. The four defects are a ventricular septal defect (VSD), pulmonary stenosis, a misplaced aorta and a thickened right ventricular wall (right ventricular hypertrophy). They usually result in a lack of oxygen-rich blood reaching the body.
What is tetralogy of Fallot repair?
Corrective repair of tetralogy of Fallot involves closure of the ventricular septal defect with a synthetic Dacron patch so that the blood can flow normally from the left ventricle to the aorta.
How do you remember tetralogy of Fallot?
A helpful mnemonic to recall these features is “PROV”. The four components of TOF is thought to result from a single defect: anterior malposition of the infundibular septum. Hypoxemic spells, also known as “Tet spells”, is a hallmark of severe TOF.
What is the pathophysiology of tetralogy of Fallot?
Tetralogy of Fallot involves a large ventricular septal defect (VSD), right ventricular outflow tract and pulmonary valve obstruction, and over-riding of the aorta. Pulmonary blood flow is decreased, the right ventricle hypertrophies, and unoxygenated blood enters the aorta via the VSD.
What is Fallot Pentalogy?
Pentalogy of Fallot is a term used to describe an association of Tetralogy of Fallot (TOF) with an atrial septal defect. 1. TOF is the most common form of cyanotic congenital heart disease and accounts for 5% to 10% of all congenital heart diseases (CHDs), with an incidence of 3 in 10000 live births.
What is pink Tetralogy Fallot?
Pink tetralogy of Fallot refers to a tetralogy of Fallot in which the degree of right ventricular outflow obstruction is minimal, resulting no significant right to left shunt, and therefore no cyanosis. Symptoms are mild and presentation may be delayed, even into adulthood.
How rare is pentalogy of Cantrell?
The exact prevalence is unknown, but estimated to be 5.5 in 1 million live births. The symptoms of pentalogy of Cantrell are present at birth (congenital).